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KMID : 0360220160570071159
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Journal of the Korean Ophthalmological Society
2016 Volume.57 No. 7 p.1159 ~ p.1164
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A Case of Lacrimal Gland MALT Lymphoma in a Patient with Primary Sjogren’s Syndrome
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Kim Hyo-Won
Sung Yoon-Mi
Paik Ji-Sun
Yang Suk-Woo
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Abstract
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Purpose: To report a case of lacrimal gland mucosa-associated lymphoid tissue (MALT) lymphoma in a patient with primary Sjogren’s syndrome and Behcet’s disease.
Case summary: A 49-year-old female patient with primary Sjogren’s syndrome and Behcet's disease presented with a one-year history of painless upper and lower eyelid swelling in her right eye. Lacrimal gland incisional biopsy was performed, and the patient was diagnosed with malignant lymphoma (extranodal marginal zone B cell lymphoma of MALT). No distant metastases were detected on whole-body computed tomography or positron emission tomography, and the patient was treated with Rituximab, Cyclophosphamide, Vincristine, Prednisone (R-CVP) regimen chemotherapy. After 8 consecutive chemotherapy cycles, her eyelids appeared normal externally, and partial regression was found radiologically.
Conclusions: The possibility of MALT lymphoma should be considered as a differential diagnosis if patients with autoimmune diseases such as primary Sjogren’s syndrome show eyelid swelling or palpable mass.
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KEYWORD
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Autoimmune disease, Behcet’s disease, Lymphoma of lacrimal gland, Mucosa-associated lymphoid tissue (MALT) lymphoma, Sjogren’s syndrome
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